Familial Presentation of Dentin Dysplasia Type-I in siblings: A Case report.

Abstract

Dentin dysplasia is a rare genetic condition with autosomal inheritance. In this case study, we report a male and female patient who are siblings, diagnosed with dentin dysplasia type I. They were the first affected generations in their family. The diagnosis of dentin dysplasia type I was confirmed based on the clinical and radiographic features. Dentin dysplasia I has distinctive radiographic features that differentiate it from other dentin developmental disorders. Since periodontitis and root morphology can cause early exfoliation of teeth, the goal is to provide preventive treatment for optimal oral function